Study Overview:

This is an open-label study designed to evaluate the long-term safety, tolerability, pharmacokinetics (PK), pharmacodynamics (PD), and clinical effects of long-term daily subcutaneous (SC) administration of nomlabofusp, also known as CTI-1601, in subjects with Friedreich’s ataxia (FRDA). 

This open label study is recruiting both individuals who have previously participated in a nomlabofusp study and individuals who have not previously participated in a nomlabofusp study.  If you or your child have not previously participated in a nomlabofusp study and are interested in joining this open label study, register through this pre-screening questionnaire to determine if you may be eligible: https://www.larimarolestudy.com/OLE

Pre-screening registration will be limited to a set number of respondents so you are encouraged to complete the questionnaire as soon as possible.

The objectives of this open label study are:

  • To evaluate the safety of long-term subcutaneous (SC) administration of nomlabofusp in subjects with FRDA
  • To evaluate the PK of long-term subcutaneous (SC) administration of nomlabofusp in subjects with FRDA
  • To evaluate the effect of long-term subcutaneous (SC) administration of nomlabofusp in subjects with FRDA on:
    • Tissue FXN concentrations
    • Clinical evaluations of FRDA
    • Gene expression and select lipids

Anyone considering participating in a clinical trial should discuss the matter with their physician. FARA does not endorse or recommend any particular studies.

Study Details:

Key Inclusion Criteria:

  • Subjects with FRDA over the age of 12 years who previously completed participation in a study of nomlabofusp who have not experienced a serious or significant adverse event during a previous nomlabofusp study or an adverse event considered clinically significant by the sponsor, or withdrawn from participation in a previous nomlabofusp for any reason
    -OR- Subjects with FRDA between the ages of 2-60 years who have not previously participated in a nomlabofusp study.
  • Subject has an HbA1c less than or equal to 7.0%.
  • Subject must demonstrate sufficient dexterity and visual acuity to prepare and self-administer daily subcutaneous injections of nomlabofusp or be able to identify a caregiver who will be trained and committed to prepare and administer the daily injections.
  • Subject resides in the United States.
  • For subjects taking or considering taking commercially available omaveloxolone (ages 16 and up):
    • Subjects currently taking omaveloxolone must have been on a stable dose for 3 months.
    • Subjects who intend to take omaveloxolone in the future must first be on a stable dose of nomlabofusp for 3 months before starting omaveloxolone.

Key Exclusion Criteria:

  • Subjects who are confirmed as compound heterozygous (GAA repeat expansion on only one allele) for FRDA.
  • Subject has any condition, disease, or situation, including a cardiac condition or disease, that in the opinion of the investigator, could confound the results of the study or put the subject at undue risk, making participation inadvisable.
  • Subject used any investigational drug or device within 90 days prior to screening.
  • Subject has a screen echocardiogram left ventricular ejection fraction (LVEF) less than 45%.

Additional inclusion and exclusion criteria apply and will be evaluated through the pre-screening questionnaire and by a study doctor. 

To pre-screen for the study, interested individuals who have not previously participated in a nomlabofusp study should fill out this pre-screening questionnaire: https://www.larimarolestudy.com/OLE

Interested individuals who have previously participated in nomlabofusp study should contact their study coordinator.

Participating Study Locations

Institution Name and LocationAge RangeSite Contacts

University of California Los Angeles
Los Angeles, CA

2 years old – 60 years old

University of Florida
Gainesville, FL

18 years old and older

Active, but not recruiting

University of South Florida
Tampa, FL

18 years old and older

Contact : Kayla Zayas
813-974-5909  Kaylazayas@usf.edu

Contact : Lucretia Campbell
813-974-5909  lcampbel@usf.edu

University of Iowa
Iowa City, Iowa

18 years old and older

Clinilabs Drug Development Corporation
Eatontown, NJ

18 years old and older

Ohio State University
Columbus, OH

18 years old and older

Active, but not recruiting

Hospital of the University of Pennsylvania
Philadelphia, PA

2 years old – 60 years old

Contact : David Lynch, MD, PhD
215-590-2242  lynchd@pennmedicine.upenn.edu

Contact : McKenzie Wells, MS
267-426-9608 wellsm@chop.edu

Uncommon Cures
Chevy Chase, MD

2 years old – 60 years old

Contact : Rachael Batabyal, MD
240-858-4938 Rbatabyal@uncommoncures.com

Contact : Tam Roshan Lal, MB, ChB
240-858-4912  troshanlal@uncommoncures.com

Explore the FA Drug Development Pipeline

FARA believes that there are many different approaches to treating Friedreich’s ataxia, and that it will require a cocktail approach of two or more treatments to slow, stop, reverse, and cure FA. Learn more about the approach behind this potential treatment and explore the other approaches that are in the FA Drug Development pipeline.